Chronic thromboembolic pulmonary hypertension, a rare complication of acute pulmonary embolism, is characterized by fibrothrombotic obstructions of large pulmonary arteries combined with small-vessel arteriopathy. It can be cured by pulmonary endarterectomy, and can be clinically improved by medical therapy in inoperable patients. A European registry was set up in 27 centers to evaluate long-term outcome and outcome correlates in 2 distinct populations of operated and not-operated patients who have chronic thromboembolic pulmonary hypertension.A total of 679 patients newly diagnosed with chronic thromboembolic pulmonary hypertension were prospectively included over a 24-month period. Estimated survival at 1, 2, and 3 years was 93

作者：Marion, Delcroix；Irene, Lang；Joanna, Pepke-Zaba；Pavel, Jansa；Andrea M, D'Armini；Repke, Snijder；Paul, Bresser；Adam, Torbicki；S?ren, Mellemkjaer；Jerzy, Lewczuk；Iveta, Simkova；Joan A, Barberà；Marc, de Perrot；Marius M, Hoeper；Sean, Gaine；Rudolf, Speich；Miguel A, Gomez-Sanchez；Gabor, Kovacs；Xavier, Ja?s；David, Ambroz；Carmen, Treacy；Marco, Morsolini；David, Jenkins；Jaroslav, Lindner；Philippe, Dartevelle；Eckhard, Mayer；Gérald, Simonneau

来源：Circulation 2016 年 133卷 9期